Epidermolysis Bullosa

Acceptability at Recruitment

ACCEPTABLE

Acceptability at CT / Work-Up

ACCEPTABLE

Individual at Risk

Donor

Explanation of Condition

Inherited disorder where skin becomes very fragile after minor trauma or friction due to a defect in attachment within the skin layers. It produces hemorrhagic blisters and subsequent broken skin, that can lead to anaemia.

Guidance

Unacceptable if patients develop blisters easily, mainly in the upper arms and trunk (injection site for G-CSF) and/or lower back (for BM harvest). Also if develops anaemia and haemoglobin drops below the acceptable cut-off value.

If small blisters located in areas such as lower limbs and normal haemoglobin, proceed.

Version

Version 1, Edition 1

Date of Last Update

15th June 2012